Sickle Cell Disorder is found in Africans, Turks, Greeks, Saudi Arabians, Egyptians, Iranians, Italians, Latin Americans and Asiatic Indians.
The Sickle Cell trait is present in 1 in 4 West Africans, 1 in 10 African-Caribbean, 1 in 10 Greeks and 1 in 50 Asians. It can also be found in 1 in 1000 White British. Beta Thalassaemia trait is found in 1 in 7 Greek Cypriots and 1 in 12 Turkish. It is less frequent in Asian, African-Caribbean and White British. 13000 people have full-blown sickle-cell in the UK; 300,000 new sickle babies are born worldwide every year.
According to WHO report of 2006 over 100.000 people in Cameroon suffer from sickle cell disease
- Each year over 10,000 babies are born with sickle cell disease in Cameroon
- Each year many children & adults will die: 80% before their 5th birthday.
- Each year hundreds of children & adults will be left disabled or chronically sick.
- Each year hundreds of people living with SCD will spend months in hospital (if they can afford it) or isolated at home
Two preventive tools
Two preventive tools are the prophylaxis with penicillin to prevent infections and transcranial Doppler scanning to identify children with an augmented risk of suffering a stroke and include them in a transfusion program. Education and psychological support, as well as a yearly checkup, will lead to a better management of the SCD.Pain, acute chest syndrome, infections, acute Anaemia and stroke may complicate the course of the disease. These complications may occur together and be difficult to disentangle, a painful crisis frequently causing fever for instance. Guidance for a correct identification of the problem and a proper use of treatments is detailed in the article.